2 结果
2.1 16例患者行直接免疫荧光法和间接免疫荧光法两种检查,且已查到详细的病历资料,见表1。其 中男性(M)5人,女性(F)11人;年龄37岁至90岁不等,平均年龄72岁;单纯结膜受累(C)9例,合并皮肤(S)或口腔(O)粘膜受累7例;临床分级均在Ⅱ级以上。
直接免疫荧光法证实结膜上皮细胞基底膜上有免疫复合物呈线状沉积(主要是IgG,其次为IgA,C3,IgM)有6例,阳性率占37.5%。
表1 16例DIF与IIF检查结果一览
Tab.1 The results of DIF and IIF in 16 cases
No. |
Sex |
Age |
Stage |
Diagnosis |
Tissue |
DIF |
IIF |
R |
L |
Conjunctiva |
Esophagus |
Conjunctiva |
IgA |
IgG |
IgM |
C3 |
IgA |
IgG |
IgM |
IgA |
IgG |
IgM |
1 |
M |
37 |
IIAIIIA1 |
IIAIIIA1 |
CP |
C+S |
- |
- |
- |
+ |
- |
- |
- |
- |
BMZ+ |
- |
2 |
F |
66 |
IIBIIA2 |
IIAIIIA2 |
CP |
C+S |
++ |
++ |
- |
- |
- |
- |
- |
- |
IIS+ |
- |
3 |
M |
74 |
IIAIIIA2 |
IIAIIIA1 |
OCP |
C |
++ |
++ |
+ |
- |
- |
- |
- |
- |
- |
- |
4 |
F |
67 |
IIAIIIB3 |
IICIIIA1 |
OCP |
C |
- |
+ |
- |
- |
- |
IIS++ |
- |
- |
IIS+ |
- |
5 |
M |
83 |
IIDIIIA2 |
IIDIIIA2-B3 |
CP |
C+S |
+ |
++ |
- |
++ |
- |
BMZ+/- |
- |
- |
- |
- |
6 |
F |
73 |
IIAIIIA1 |
IIAIIIA2 |
OCP |
C |
- |
- |
- |
- |
- |
- |
- |
- |
- |
- |
7 |
M |
82 |
IIAIIIA1 |
IIBIIIA1 |
OCP |
C |
- |
- |
- |
- |
- |
BMZ++
IIS++ |
- |
- |
IIS+
BMZ+/- |
- |
8 |
F |
61 |
IICIIIA1 |
IIBIIIA3 |
OCP |
C |
- |
- |
- |
- |
- |
IIS++ |
- |
- |
IIS++ |
- |
9 |
F |
78 |
IIAIIIA-B |
IIA2 |
CP |
C+S |
- |
- |
- |
- |
- |
- |
- |
BMZ+ |
BMZ++ |
- |
10 |
F |
72 |
IV |
IIA |
OCP |
C |
- |
- |
- |
- |
- |
- |
- |
- |
- |
- |
11 |
F |
90 |
IIBIIIB3 |
IICIIIB3 |
OCP |
C |
- |
- |
- |
- |
- |
BMZ++ |
- |
IIS+ |
IIS ++ |
- |
12 |
F |
72 |
IIBIIIB1 |
IICIIIB2 |
OCP |
C |
- |
- |
- |
- |
- |
IIS+ |
- |
- |
- |
- |
13 |
F |
69 |
IIBIIIA1 |
IICIIIB3 |
CP |
C+O |
+ |
++ |
- |
- |
- |
- |
- |
- |
- |
- |
14 |
M |
83 |
IICIIIB3 |
IICIIIB2 |
OCP |
C |
- |
- |
- |
- |
- |
- |
- |
- |
- |
- |
15 |
F |
75 |
IIBIIIC4 |
IIAIIIB2 |
CP |
C+S |
- |
- |
- |
- |
- |
IIS+ |
- |
- |
IIS+ |
- |
16 |
F |
70 |
IIBIIB |
IICIIIA1 |
CP |
C+S |
+ |
+ |
- |
+ |
- |
BMZ+ |
- |
BMZ+ |
BMZ++ |
- |
间接免疫荧光法检测血清中抗基底膜(basement membrane zone,BMZ)抗体阳性3例(18.7%),抗细胞间基质(intraepithelial intercellular substance,IIS)抗体阳性6例(37.5%),主要是IgG,其次为IgA,总阳性率为56.25%。
直接免疫荧光法与间接免疫荧光法间无明显对应关系。
2.2 34例病人行人结膜和鼠食道为基质的间接免疫荧光检查,男性10例,女性24例,以结膜为基质的血清中抗基底膜抗体阳性4例(11.76%),抗细胞间物质抗体阳性14例(41.17%),总阳性率为52.9%,主要是IgG,其次是IgA,而IgM均为阴性。以鼠食道为基质的阳性率为38.2%,阳性间有一定的对应关系。
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